A rare disorder in which the veins draining blood from the liver become blocked or narrowed. Blood accumulates in the liver, which swells. Liver failure and portal hypertension result. Treatment is aimed at removing the cause of the obstruction: this may be a blood clot, pressure on the veins from a liver tumour, or a congenital abnormality of the veins. In most cases, treatment has only a limited effect and, unless a liver transplant can be done, the disease is fatal within 2 years.
Budd–Chiari syndrome |
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